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[ioEA1004] ioGlutamatergic Neurons HTT 50CAG/WT
제품코드 : ioEA1004
제품정보 : ioGlutamatergic Neurons HTT 50CAG/WT
Human iPSC‑derived Huntington’s disease model
A rapidly maturing, physiologically relevant, functional system to study Huntington’s disease (HD). This in vitro HD cell model shows reduced neuronal network activity, decreased spontaneous activity, and mitochondrial dysfunction compared to the genetically matched control.
ioGlutamatergic Neurons HTT 50CAG/WT are opti‑ox deterministically programmed excitatory neurons containing a genetically engineered heterozygous 50 CAG trinucleotide repeat expansion in exon 1 of the huntingtin (HTT) gene.
Applications: Huntington’s disease research, Drug discovery, Disease modelling, MEA analysis, Seahorse assays